Unsuspected Ganglioneuroma of the Choroid Diagnosed after Enucleation.

نویسندگان

  • Michael Mbagwu
  • Bahram Rahmani
  • Arth Srivastava
  • Delilah Burrowes
  • Paul J Bryar
چکیده

We report a case of an unsuspected ganglioneuroma of the choroid in a patient with neurofibromatosis type 1. A 5-year-old girl presented from an outside institution with right proptosis and glaucoma since birth. Magnetic resonance imaging was obtained and showed a cavernous sinus mass extending into the right orbit and multiple orbital lesions. Additionally, increased signal in the posterior globe of the right eye was noted, but its etiology was unclear at the time. She was lost to follow-up for 3 years and later returned with a blind painful eye. Enucleation was performed, and histopathology was significant for diffuse choroidal ganglioneuroma and advanced glaucoma. We report the atypical history, examination findings, and histopathology to support the diagnosis.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Malignant melanoma of the choroid in a husband and wife.

A 52-year-old man was diagnosed as having a large malignant melanoma of the choroid in the right eye. Six years later his 58-year-old wife of almost 40 years was diagnosed as having a large malignant melanoma of the choroid in her left eye. In both patients the diagnosis was confirmed histologically following enucleation. Electron microscopy failed to reveal evidence of viral particles within t...

متن کامل

Local recurrence of choroidal malignant melanoma following enucleation.

542 cases of choroidal malignant melanoma were reviewed. Local recurrence occurred in only 6 patients (1.11%). Five of the 6 patients had distant metastases when the local recurrence was diagnosed, and the remaining patient also developed metastases after a passage of time. These figures do not support the concept of withholding a primary implant at the time of enucleation.

متن کامل

Metastasis rates and sites after treatment for choroidal melanoma by proton beam irradiation or by enucleation

PURPOSE To investigate tumor thickness and location, the interval of time between treatment for choroidal melanoma (proton beam irradiation or enucleation) and diagnosis of metastatic disease, and rates and sites of metastasis. DESIGN Retrospective, interventional, noncomparative case series. METHODS Follow-up of 152 patients with primary choroidal melanoma, between 1992 and 2006 (14 years)...

متن کامل

Enhanced Wound Healing after Leiomyoma Enucleation

Leiomyoma is a rare esophageal tumor that constitutes less than 1% of esophageal malignancies. It should be removed when diagnosed even if asymptomatic. This study presents two cases of esophageal leiomyoma in 38 and 62 years old men who presented with dysphagia and evaluated for diagnosis and location of related tumors. Patients were clinically examined and upper gastrointestinal endoscopy, ch...

متن کامل

Uveal Melanoma.

BACKGROUND: Malignant melanoma of the uveal tract is a rare malignancy but a significant cause of mortality and visual loss. Approximately 50% of patients diagnosed with a melanoma of the choroid or ciliary body will die of the disease within 15 years of enucleation. METHODS: The author reviewed the current literature on the clinical findings, epidemiology, and treatment of uveal melanoma. RESU...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • Ocular oncology and pathology

دوره 2 1  شماره 

صفحات  -

تاریخ انتشار 2015